СИНДРОМ УДЛИНЕННОГО ИНТЕРВАЛА QT. ЧАСТЬ 1

  • Л. В. Колоцей УЗ «Гродненская областная клиническая больница»
  • В. А. Снежицкий УО «Гродненский государственный медицинский университет» http://orcid.org/0000-0002-1706-1243

Аннотация

Синдром удлиненного интервала QT (LQTS) – это потенциально жизнеугрожающая каналопатия, сопровождающаяся удлинением интервала QT на 12-канальной ЭКГ, синкопальными состояниями и высоким риском внезапной сердечной смерти вследствие развития полиморфной желудочковой тахикардии типа torsade de pointes. Первоочередная цель в ведении пациентов с LQTS на современном этапе состоит в недопущении недиагностированных его форм, адекватном лечении и профилактике, чему способствует быстрое развитие молекулярной биологии и генетики. В первой части настоящего обзора отражена история изучения, этиология, эпидемиология, патогенез и клиническая картина синдрома удлиненного интервала QT.

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2018-09-07
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Колоцей ЛВ, Снежицкий ВА. СИНДРОМ УДЛИНЕННОГО ИНТЕРВАЛА QT. ЧАСТЬ 1. Журнал ГрГМУ (Journal GrSMU) [Интернет]. 7 сентябрь 2018 г. [цитируется по 8 декабрь 2022 г.];16(4):388-93. доступно на: http://journal-grsmu.by/index.php/ojs/article/view/2292

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